Журнал включен в российские и международные библиотечные и реферативные базы данных
РИНЦ (Россия)
RINZ (RUSSIA)
Регистрационное агентство DOI (США)
DOI Registration Agency (USA)
Эко-Вектор (Россия)
Eco-Vector (Russia)
Ulrichsweb (Ulrich’s Periodicals Director

Congenital epidermolysis bullosa in medical practice

DOI: https://doi.org/10.29296/25879979-2021-03-07
Download full text PDF
Issue: 
3
Year: 
2021

1. Vsevolod V. Skvortsov, Dr. of Sciences (Medical), Associate Professor, Internal Medicine Department, Volgograd state medical university, Russian Health Ministry, [email protected] 2. Galina V. Eremina, Assistant of the Department of Skin and Venereal Diseases, Volgograd state medical university, Russian Health Ministry [email protected] 3. Elena V. Belyakova, PhD in Medical Sciences, Assistant of the Internal Medicine Department, Volgograd state medical university, Russian Health Ministry, [email protected] 4. Andrey A. Eremenko, student, Volgograd state medical university, Russian Health Ministry, [email protected] 5. Yasko Natalya Vladimirovna, 5th year student, General Medicine Department, Volgograd state medical university, Russian Health Ministry [email protected]

Congenital bullous epidermolysis is a disease characterized by recurrent blistering as a result of structural weakness, fragility of the skin and some other tissues. Today, there are a number of criteria for the diagnosis, diagnosis and treatment of this pathology. The article tells about the main strongholds for general practitioners and dermatovenerologists who are faced with this disease.

Keywords: 
congenital bullous epidermolysis
classification
clinic
symptoms
diagnosis
treatment



It appears your Web browser is not configured to display PDF files. Download adobe Acrobat или click here to download the PDF file.

References: 
  1. Dermatovenerologija. Natsional'noe rukovodstvo. Pod red. Ju.K. Skripkina, Ju.S. Butova, O.L. Ivanova. M.: GEOTAR-Media, 2011, 1024 s.
  2. Dermatovenerologija. Pod red.A.A. Kubanovoj. M.: DEKS-PRESS, 2010, 28 s.
  3. Chebotarev V.V., Bajda A.P. Rukovodstvo dlja vrachej obschej praktiki (semejnyh vrachej) po dermatovenerologii. Stavropol': Sed'moe nebo, 2009, 328 s.
  4. Krouchuk D.P., Manchini A. Dzh. Detskaja dermatologija: spravochnik. Per. s angl. pod red. N.G. Korotkogo. M.: Prakticheskaja meditsina, 2010, 608 s.
  5. Bulleznye dermatozy (voprosy kliniko-morfologicheskoj diagnostiki i morfogeneza po dannym elektronnoj i atomnosilovoj mikroskopii). Pod red. V.I. Prohorenkova, A.A. Gajdasha, L.N. Sinitsy. Krasnojarsk: IPTs «KASS», 2008, 188 s.
  6. Grehem-Braun R. i dr. Prakticheskaja dermatologija. per. s angl. pod red. N.M. Sharovoj. M.: MedPress-inform, 2011, 360 s.
  7. Evropejskoe rukovodstvo po lecheniju dermatologicheskih zabolevanij: per. s angl. Pod red. A.D. Kasambasa, T.M. Lotti, M.: MedPress-inform, 2008, 736 s.
  8. Klinicheskaja dermatovenerologija: v 2-h t. / Pod red. Ju.K. Skripkina, Ju.S. Butova, M.: GEOTAR-Media, 2009.
  9. Klinicheskie rekomendatsii dlja vrachej, okazyvajuschih mediko-sanitarnuju pomosch'. Kozhnye bolezni. - M.: Meditsina Shiko, 2008, 544 s.
  10. Jusupova L.A., Junusova E.I., Garaeva Z.Sh., Mavljutova G.I., Morozova M.A. Sovremennye osobennosti kliniki, diagnostiki i terapii bol'nyh bulleznym epidermolizom, M.: Lechaschij vrach №1, 2018, s. 71-74.
  11. Epishev R.V. Nutritivnaja podderzhka detej s vrozhdennym bulleznym epidermolizom. – Dissertatsija na soiskanie uchenoj stepeni kandidata meditsinskih nauk, Moskva, 2018, .17.
  12. Serdjukova E.A., Popov V.V. Lechenie vrozhdennogo bulleznogo epidermoliza u detej. Lekarstvennyj vestnik, № 4, 2016, s.44-46.
  13. Tlish M., Kartashevskaja M. Autodestruktivnyj dermatoz kak aktual'naja mezhdistsiplinarnaja problema . Vrach, 2018; (4): 32-35 https://doi.org/10.29296/25877305-2018-04-05
  14. Potekaev N., Trahtman P., Rassohina O., Shuginina E., Ivanova L. Kozhnaja toksichnost' himioterapii i kozhnye projavlenija hronicheskoj reaktsii «transplantat protiv hozjaina». printsipy nemedikamentoznoj korrektsii porazhenij kozhi. Vrach, 2017; (8): 8-14
  15. Korostelev M., Korostelev A., Shihaleva N. Sravnitel'naja harakteristika metodov fiksatsii kozhnyh transplantatov. Vrach, 2016; (11): 84-87
  16. Rassohina O., Shuginina E., Trahtman P., Potekaev N. Algoritm dermatoskopicheskogo issledovanija sosudov nogtevogo valika bol'nyh s kozhnymi projavlenijami hronicheskoj reaktsii transplantat protiv hozjaina dlja vrachej obschej praktiki. Vrach, 2017; (7): 43-46
  17. Sherina T. Mar'janovskij A. Ispol'zovanie kompleksnyh bioreguljatsionnyh preparatov v vosstanovitel'nom lechenii atopicheskogo dermatita. Vrach, 2017; (12): 70-73